Case of Juvenile Nasopharyngeal Angioma

  • A 24 years male brought by relatives in COLLAPSE STATE WHICH WAS EXPECTED TO DIE WITHIN JUST FEW DAYS……MALIGNANT ANGIOFIBROMA WITH POOR PROGNOSIS……COLLAPSE.
  • NOW NORMAL SINCE 5 YEARS
  • HISTORY—Came with the diagnosis of Angiofibroma with intracranial extension with recurrence, operated thrice again Recurred—took to GMC — All Surgeons Refused Surgery – Pt left to Die. Doctor said that he was in worst condition with brain involvement and he will not live long, die at any time. After that came in clinic as last hope in semi comatose condition, disoriented with toxic look.
  • A Case of JUVENILE Naso-Pharyngeal Angiofibroma with Intracranial Extension with Seizure Disorder
  • brought with following S/s
  • Convulsions,
  • Stuporous state , unable to recognize the things,peoples
  • Ataxia of both legs , Unable to walk/sit/talk
  • Tendency to fall on right side,
  • Sleep disturbed

 Final Diagnosis

  • OPERATED CASE  OF  LARGE  JUVENILE NASO-PHARYNGEAL   ANGIOFIBROMA  GRADE-3  WITH  INTRACRANIAL  EXTENSION WITH  SEIZURE  DISORDER  WITH ATAXIA  WITH 

Three Surgeries Done

  • First:- A Naso-Pharyngeal Mass Removed
  • Second:- Recurrence with Intracranial Extension. Intranasal Surgery Done
  • Third: – Again Recurrence with Gross Intracranial Involvement. Surgery done through opening the skull vault and Intranasal Route– Pt got Critical during surgery and saved with difficulty–took very long time to recover but was never normal thereafter.

Surgeons Advice:-

  • After operating thrice, Doctor said that he was in worst condition with brain involvement and he will not live long, die at any time and so that relatives lost hope for him.
  • Again Recurred—took to GMC — All Surgeons Refused Surgery – Pt left to Die

Last Hope

  • As a Last Hope Patient was brought to our Clinic being Carried by Three Relatives, almost lifting him and kept him on bed:-
  • Disoriented, Drowsy,
  • Swollen, Bleeding Gums
  • Toxic Look, GC Very Poor
  • Unable to Talk
  • LIFE HISTORY:
  • He was very irritable, obstinate never obey others.
  • Once decided than never listen to anybody.
  • Not so interested in studies.
  • Scolded by his mother due to bunking the school and for eating clay.
  • He used to play with coins and mostly like new currency, new coin and new 500rs note ,if currency note is slightly old or cut than has to change that note.
  • He was attracted toward the new things or animals like dog, cat, rat etc.
  • He like those animal or buffalo which is more powerful & strong, fighter bull.
  • He is a shep.
  • herd, goes to rear cattle but wants to be tip top always.
  • He always likes perfect dressing. He went out of the home in good dressing only.
  • He wants every thing neat & clean and in order.
  • He is intellectually dull , not so mature but must dressing like a gentleman.

Follow Up

  • After 1 month:-
  • Collapse  State Improved Gradually
  • Epistaxis >+++
  • Appetite Improved
  • Ataxia >
  • Appetite Better
  • Convulsions >++
  • Patient Started improvement within 1 day with TOXIC LOOK and ATAXIA & COLLAPSE SHOWING IMPROVEMENT.
  • After 2 Months
  • All Improving
  • Convulsions >
  • Ataxia >
  • No Epistaxis
  • After 6 Months
  • All Improving
  • Convulsions >
  • Ataxia >; Walking with support
  • No Epistaxis
  • Comprehension better
  • Understanding >
  • After 1 year:-
  • Walking ,talking well
  • understanding better
  • No Epistaxis
  • Anticonvulsions much reduced

A BOY who was left to die within few days NOW SINCE 5 YEARS ALMOST NORMAL DOING ALL HIS REGULAR WORK WITH OCCASIONAL CONVULSIONS .